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Amylopectinosis
Amylopectinosis brancher deficiency
Andersen disease
Andersen's disease
Brancher deficiency
Brancher enzyme deficiency
Dextrinosis
Familia
GSD IV
Gierke's disease
Glycogen
Glycogen disease
Glycogen starch synthase
Glycogen storage disease
Glycogen storage disease I
Glycogen storage disease type IV
Glycogen synthase
Glycogenopathy
Glycogenoses
Glycogenosis
Glycogenosis IV
Hepatorenal glycogenosis
Liver glycogen
Muscle glycogen
Najjar-Andersen syndrome
Re-fuelling of glycogen stores
Recovery of glycogen stores
Type 1 glycogenosis
Type I glycogen storage disease
Von Gierke's disease

Übersetzung für "glycogen " (Englisch → Französisch) :

TERMINOLOGIE
glycogen storage disease [ glycogen disease | glycogenosis ]

glycogénose


glycogen synthase | glycogen starch synthase

glycogène synthase


type I glycogen storage disease [ von Gierke's disease | Gierke's disease | type 1 glycogenosis | glycogen storage disease I | hepatorenal glycogenosis ]

maladie de von Gierke [ glycogénose de type I | glycogénose hépato-rénale ]




glycogen storage disease | glycogenosis | glycogenopathy | dextrinosis | glycogenoses

glycogénose | thésaurose glycogénique | glycogénoses






recovery of glycogen stores | re-fuelling of glycogen stores

restauration de la réserve en glycogène | récupération de la réserve en glycogène


An extremely rare genetic glycogen storage disease reported in one patient to date. Clinical signs included muscle weakness, cardiac arrhythmia associated with accumulation of abnormal storage material in the heart and glycogen depletion in skeletal

glycogénose avec cardiomyopathie sévère par déficit en glycogénine


Andersen's disease [ Andersen disease | Najjar-Andersen syndrome | glycogenosis IV | glycogen storage disease type IV | GSD IV | alpha 1,4-glucan-6-glucosyl transferase deficiency | amylopectinosis brancher deficiency | brancher enzyme deficiency | brancher deficiency | amylopectinosis | familia ]

maladie d'Andersen [ glycogénose musculaire type IV ]
IN-CONTEXT TRANSLATIONS
Vitamin B6 contributes to normal protein and glycogen metabolism

La vitamine B6 contribue au fonctionnement normal du système immunitaire


Vitamin B6 contributes to normal protein and glycogen metabolism

La vitamine B12 contribue au métabolisme normal de l’homocystéine


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